RESUMO
Sturge-Weber syndrome (SWS) includes facial, leptomeningeal and choroidal hemangioma. The retinal vasculature is essentially normal. Rare cases of retinal vascular tortuosity and arterio-venous malformations have been reported. We report two cases with rare concomitant retinal vascular abnormalities along with SWS. Both the patients had nevus flammeus, hemifacial hypertrophy, and choroidal hemangioma. In one case, retinal cavernous hemangioma was seen in the affected eye. The other case revealed retinal neovascularization secondary to proliferative diabetic retinopathy in the eye with choroidal hemangioma.
Assuntos
Neoplasias da Coroide/etiologia , Hemangioma/etiologia , Descolamento Retiniano/etiologia , Doenças Retinianas/etiologia , Vasos Retinianos/patologia , Síndrome de Sturge-Weber/complicações , Neoplasias da Coroide/diagnóstico , Angiofluoresceinografia , Fundo de Olho , Hemangioma/diagnóstico , Humanos , Masculino , Pessoa de Meia-Idade , Descolamento Retiniano/diagnóstico , Doenças Retinianas/diagnóstico , Tomografia de Coerência Óptica , Adulto JovemRESUMO
To report a case of peripheral exudative hemorrhagic chorioretinopathy (PEHCR) associated with extramacular choroidal neovascular membrane (CNVM). A 65-year-old female with BCVA of 3/60 in the RE was diagnosed to have PEHCR with peripheral CNVM. She had subretinal fluid in the macular region. The patient was treated successfully with a single dose of intravitreal bevacizumab followed by laser photocoagulation of the CNVM. BCVA was 6/24 after 3 months and subretinal fluid had resolved. PEHCR may be associated with extramacular CNVM and hence may cause visual loss. Such extramacular CNVMs respond well to combination therapy which offers a permanent cure.
